What are the Treatment Options for Denys-Drash Syndrome?
Treatment for DDS is multidisciplinary and often involves the following approaches:
Management of nephrotic syndrome: This may include the use of diuretics, steroids, or immunosuppressive agents to control proteinuria and edema. Surgical intervention: Removal of Wilms tumor and potentially affected kidney tissue is often necessary. Hormone therapy and surgical correction: For individuals with ambiguous genitalia, hormone replacement therapy and surgical correction may be considered. Regular monitoring: Continuous follow-up with a pediatric nephrologist and oncologist is essential for managing complications and monitoring for the recurrence of Wilms tumors.
