The treatment for GSDs is tailored to the specific type and severity of the disease and aims to manage symptoms and prevent complications: - Dietary Management: Frequent feeding with cornstarch or other complex carbohydrates to maintain blood glucose levels, especially in GSD Type I. - Enzyme Replacement Therapy (ERT): Available for Pompe disease to replace the deficient enzyme. - Medications: To manage complications like hyperuricemia or hyperlipidemia. - Liver Transplantation: Considered in severe cases with liver failure or hepatocellular carcinoma risk.
