What are the Treatment Options for Desmosomal Disorders in Pediatrics?
Treatment strategies for desmosomal disorders in pediatric patients are often tailored to the specific condition and its severity.
Topical and Systemic Therapies: Used to manage skin conditions like Epidermolysis Bullosa and Pemphigus Vulgaris. Cardiac Management: For conditions like ARVC, treatment may include medications, lifestyle changes, and in some cases, surgical interventions such as implantable cardioverter-defibrillators (ICDs). Genetic Counseling: Provides families with information about the hereditary nature of these disorders, supporting informed decision-making.